Turcot's syndrome, the association of brain tumor (usually glioblastoma, medullo‐blastoma, or astrocytoma) and colonic polyps, is a very rare condition of which about 20 cases have been reported. It has been described only once previously with cancer in a third organ system. In this paper, we report a child affected with colonic polyposis and astrocytoma (i.e., Turcot's syndrome) associated with intestinal non‐Hodgkin's lymphoma. Copyright © 1990 Wiley‐Liss, Inc., A Wiley Company

Turcot's syndrome with intestinal lymphoma in a child: An unusual case of triple tumor

LOCATELLI, DAVIDE;
1990-01-01

Abstract

Turcot's syndrome, the association of brain tumor (usually glioblastoma, medullo‐blastoma, or astrocytoma) and colonic polyps, is a very rare condition of which about 20 cases have been reported. It has been described only once previously with cancer in a third organ system. In this paper, we report a child affected with colonic polyposis and astrocytoma (i.e., Turcot's syndrome) associated with intestinal non‐Hodgkin's lymphoma. Copyright © 1990 Wiley‐Liss, Inc., A Wiley Company
1990
astrocytoma; colonic polyposis; multiple tumors; Pediatrics, Perinatology and Child Health; Oncology; Cancer Research
Aricó, Maurizio; Parigi, Gian Battista; Locatelli, Davide; Bragheri, Romano; Lombardi, Fabrizio; Zangrandi, Adriano
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Utilizza questo identificativo per citare o creare un link a questo documento: https://hdl.handle.net/11383/2061300
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